From:  Urgent cesarean delivery with contingent ECPR preparation for a parturient with Eisenmenger syndrome and supra-systemic pulmonary hypertension: a case report

 Timeline of clinical events.

EventDetails/Findings
Previous pregnancy three years priorDiagnosed with pulmonary hypertension during her fourth pregnancy and underwent an emergency cesarean section. Transthoracic echocardiography (TTE) revealed a large secundum atrial septal defect (ASD) and severe pulmonary hypertension with a right ventricular systolic pressure (RVSP) of 94 mmHg.
Two weeks prior to hospital admissionPresented to an outside hospital for shortness of breath and palpitations. TTE RVSP was 105 mmHg.
Admission to labor and delivery servicePresented at 37 weeks gestation with worsening dyspnea, dizziness, and pre-syncopal episodes with exertion.
Placement of epidural catheterAfter activation of the epidural, she developed hypotension requiring vasopressor support and eventual discontinuation of the epidural.
Transfer to the intensive care unit (ICU)On vasopressor support and inhaled nitric oxide. TTE showed a 2.4 cm ostium secundum ASD with intermittent right-to-left shunting, RVSP 80 mmHg with systemic systolic pressure of 95 mmHg. A radial arterial and central venous catheter were placed.
Cesarean section deliveryEpidural incrementally loaded in the operating room. Extracorporeal cardiopulmonary resuscitation (ECPR) catheters were placed. Required vasopressin, phenylephrine, and epinephrine infusions. Her baby was delivered by cesarean section.
Post-operative day oneRemained on inhaled nitric oxide, a vasopressin infusion, and treprostinil.
Post-operative day elevenWeaned off vasoactive support. Treprostinil was continued and she was started on goal directed therapy with tadalafil, furosemide, and spironolactone. Discharged on postoperative day 11 with supplemental oxygen (2–4 L/min via nasal cannula).
Six weeks after dischargeReadmitted six weeks after discharge with a pulmonary hypertensive crisis, ventricular fibrillation arrest, and acute hypoxic respiratory failure.
Nine months after dischargeShe unfortunately passed away 9 months later due to an out of hospital cardiac arrest.