From:  Type 2 diabetes in dementia and Alzheimer’s disease: Intertwined global health issues brewing on the horizon

 Alzheimer’s disease and related dementias.

Key informationKey pathologiesMajor risk factors
Alzheimer’s disease (AD)
Most common dementia, accounting for an estimated 60 to 80% of cases [4]. Most AD (> 95%) occurs as sporadic, late-onset AD (usually > 65 years of age) without autosomal dominant inheritance of highly penetrant APP, PSEN1, PSEN2 mutations, which instead give rise to familial or autosomal dominant, early-onset AD.Extracellular amyloid-β plaques and intracellular neurofibrillary tangles of hyperphosphorylated tau protein [202]. Chronic neuroinflammation, synaptic dysfunction, and neuronal loss. Often accompanied by vascular abnormalities and mitochondrial and metabolic dysfunction.Age (strongest non-genetic factor); genetics (hallmark genes include APP, PSEN1, PSEN2, APOE4, TREM2, among others [21]); cardiometabolic risk factors (diabetes, obesity, hypertension); environmental and lifestyle risk factors.
Vascular dementia
The second most common dementia, accounting for approximately 15% of cases.Dementia caused by cerebrovascular injury from large-vessel strokes, small-vessel disease (white matter lesions, lacunes), chronic cerebral hypoperfusion [203, 204].Age; cardiometabolic risk factors (hypertension, diabetes, obesity, hyperlipidemia, stroke); environmental and lifestyle risk factors; genetics (hallmark genes include APOE4, SPRY2, FOXA2, among others [21]) as well as rare genetic forms (e.g., NOTCH3 in the most common heritable cause of stroke and vascular dementia, cerebral autosomal dominant arteriopathy with subcortical infarcts and leukoencephalopathy (CADASIL) [205]).
Lewy body dementia
Includes dementia with Lewy bodies and Parkinson’s disease dementia [206].α-Synuclein aggregates of Lewy bodies and Lewy neurites accompanied by neuronal loss.Age; genetics (hallmark genes include APOE4, SNCA, GBA, among others [21]).
Frontotemporal dementia
A leading type of early-onset dementia [207].Selective degeneration of frontal and temporal lobes. Abnormal accumulation of tau, TDP-43, or FUS proteins (depending on subtype). Neuronal loss leading to behavioral, language, or executive dysfunction.Genetics is the primary known risk factor (hallmark genes include APOE4, GRN, C9orf72, MAPT, among others [21]).
Mixed pathology dementias
A substantial proportion, possibly the majority, of dementia cases develop mixed pathology.AD neuropathology with 1, 2, and 3 other neuropathological features (microvascular brain injury, Lewy body dementia, hippocampal sclerosis, limbic predominant TDP-43 encephalopathy, cerebral amyloid angiopathy) [5, 109]. Dementia cases can also develop multiple neuropathological features without AD neuropathology.Not applicable.

APOE4: apolipoprotein E4; APP: amyloid precursor protein; PSEN1: presenilin-1; PSEN2: presenilin-2.