From:  Extracellular vesicles in neurological disorders: emerging roles and underlying molecular mechanisms

 Comparative analysis of PTMs in EV cargo selection.

PTM typeKey regulatory proteinsMolecular mechanismCargo selection specificityImpact on EV contentNeurological relevanceKey references
UBL3 modificationUBL3 (membrane-anchored ubiquitin-fold protein)Geranylgeranylation-dependent membrane anchoring promotes protein-membrane association via the C-terminal CAAX motifBroad spectrum: > 1,200 interactors; ~30% are EV cargo proteins, including Ras, α-synuclein, mHTT~60% reduction in sEV protein content upon knockoutα-synuclein (PD), mHTT (HD); interaction upregulated under oxidative stress[18, 20]
UbiquitinationESCRT-0, ALIX, TSG101, MARCH E3 ligasesRecognition of ubiquitinated membrane proteins; ESCRT complex recruitment for MVB sortingSelective for ubiquitin-tagged transmembrane proteins; MHC-II moleculesEssential for ESCRT-dependent exosome formationImmune molecule sorting; potential role in neuroinflammation[53, 54]
SUMOylationSUMO-2, SUMO-conjugating enzymesCovalent attachment of SUMO moieties facilitates ESCRT interactionshnRNPA2B1-mediated miRNA sorting via specific motifs; α-synuclein, APP sortingControls specific miRNA profiles (e.g., miR-146a) and protein aggregatesmiRNA-mediated neuroinflammation; α-synuclein propagation (PD); APP processing (AD)[58, 65]
PalmitoylationPalmitoyl acyltransferases (PATs)S-acylation with palmitate enhances hydrophobic membrane interactionsMembrane-associated proteins; tetraspanins (CD9, CD63, CD81)Governs protein-membrane dynamics and clustering in lipid raftsTetraspanin-mediated EV formation; potential role in synaptic vesicle release[57, 58]
GlycosylationGlycosyltransferasesN- or O-linked glycan addition to transmembrane proteinsSurface glycoproteins: EWI-2 and other tetraspanin partnersDetermines EV targeting, uptake specificity, and immunological recognitionBBB targeting, microglial uptake specificity, neuroimmune interactions[66]

AD: Alzheimer’s disease; APP: amyloid precursor protein; BBB: blood-brain barrier; ESCRT: endosomal sorting complex required for transport; EV: extracellular vesicle; HD: Huntington’s disease; hnRNPA2B1: heterogeneous nuclear ribonucleoprotein A2/B1; MARCH: membrane-associated RING-CH; MHC: major histocompatibility complex; miRNA: microRNA; mHTT: mutant huntingtin; MVB: multivesicular body; PD: Parkinson’s disease; PTMs: post-translational modifications; sEV: small EV; UBL3: ubiquitin-like protein 3.