From:  The association of primary biliary cholangitis with metabolic syndrome and metabolic dysfunction-associated steatotic liver disease

 Comparison of studies evaluating the impact of coexisting MASLD on disease severity and progression in PBC.

FeatureHíndi et al., 2013 [34]Minuk et al., 2018 [17]Iluz-Freundlich et al., 2021 [32]Hernández-Pérez et al., 2024 [24]Drazilova et al., 2026 [22]Del Barrio et al., 2026 [25]Ren et al., 2025 [33]
Study designRetrospective biopsy reviewRetrospective cohortRetrospective cohortRetrospective two-center cohortCross-sectionalRetrospective multicenter cohort (ColHai registry)Retrospective cohort
Sample size49 AMA-positive PBC patients168 PBC alone vs. 68 PBC/MASLD136 MASLD alone vs. 68 MASLD/PBC129 biopsy-proven PBC patients152 PBC patients469 PBC patients (158 with SLD, 124 with MASLD)363 PBC patients (87 with concurrent MASLD)
Comparison groupsPBC with MASH vs. PBC without MASHPBC alone vs. PBC/MASLDMASLD alone vs. MASLD/PBCPBC with MASLD vs. PBC without MASLDPBC patients stratified by MASLD and MetS; age/sex-matched controls used for prevalence comparisonPBC with SLD vs. PBC without SLDPBC alone vs. PBC/MASLD
MASLD definitionHistologic MASH in AMA-positive PBC biopsiesBiochemical criteria/noninvasive scoresBiochemical criteria/noninvasive scoresHistology (biopsy-proven). MASLD defined as steatosis > 5% + ≥ 1 metabolic risk factorNoninvasive imaging (TE/CAP)Imaging and/or clinical criteria (78.5% met MASLD criteria)Clinical criteria per 2023 AASLD guidelines
Outcome measuresHistological severity: ductal biliary damage, inflammationLFTs (ALP, GGT), Fib-4, APRILFTs, Fib-4, APRI, INR, albuminValidated PBC scores (Paris II, Toronto, APRI, Globe, UK PBC) at 5, 10, 15 years; liver-related mortality and transplantationTE, biochemical response to UDCAUDCA response at 1 year (Paris II, GLOBE, UK-PBC, deep response, complete normalization); liver-related eventsBiochemical response (Paris criteria); APRI, Fib-4; GLOBE score
Key findingsMASH is associated with more severe ductal damage and fibrosisPBC-alone had higher baseline activity (ALP, GGT) and severity (Fib-4); progression appeared worse in PBC-alone but not statistically significantMASLD/PBC group had lower and less deterioration of Fib-4 vs. MASLD alone at follow-upCoexisting MASLD associated with significantly worse treatment response and higher liver-related mortality/transplantation; steatosis/dyslipidemia/advanced fibrosis independently associated with worse outcomesMetS (not MASLD) independently associated with advanced fibrosis (OR 4.561); MASLD prevalence similar to controls (42.3% vs. 41.9%); neither MASLD nor MetS affected UDCA responseSLD not associated with adverse UDCA response at 1 year by any criteria or liver-related eventsBiochemical response rates similar; PBC/MASLD had lower APRI and Fib-4 after 1-year UDCA; and better predicted transplant-free survival
MASLD vs. MetS distinctionOverweight associated with advanced fibrosis, but not formally separatedNot addressedNot addressedSteatosis (not MASH) independently associated with worse outcomes after adjusting for metabolic comorbiditiesKey finding: MetS, not MASLD, drives fibrosis; each additional MetS criterion increases risk 1.9-fold78.5% of SLD patients met MASLD criteria; metabolic comorbidities noted but not independently analyzed as driverNot formally separated
Principal limitationsSmall sample, cross-sectional, no longitudinal follow-upRetrospective, single-center, disease activity assessed using biochemical markers, no histologyRetrospective, no histologyRetrospective, modest sample size (n = 129), 36% of MASLD had MASH, older age in the PBC/MASLD groupCross-sectional, no histology, cannot assess longitudinal progressionRetrospective, no histologic confirmation of SLD in most patientsRetrospective, no histology, MASLD defined clinically, single-center

ALP: alkaline phosphatase; AMA: anti-mitochondrial antibodies; APRI: AST-to-platelet ratio index; CAP: controlled attenuation parameter; Fib-4: Fibrosis-4 index; GGT: gamma-glutamyl transferase; INR: international normalized ratio; LFTs: liver function tests; MASH: metabolic dysfunction-associated steatohepatitis; MASLD: metabolic dysfunction-associated steatotic liver disease; MetS: metabolic syndrome; OR: odds ratio; PBC: primary biliary cholangitis; SLD: steatotic liver disease, TE: transient elastography; UDCA: ursodeoxycholic acid.